Aneurysmal bone cyst of thoracic spine in polyostotic fibrous dysplasia causing acute myelopathy

Bone-Grafting in Polyostotic Fibrous Dysplasia.

BACKGROUND Polyostotic fibrous dysplasia is a skeletal disease that results from somatic activating mutations in the gene GNAS in skeletal stem cells, leading to proliferation of immature osteogenic cells with replacement of normal marrow and bone with fibro-osseous tissue. Lesions may cause bone deformity or fracture. In the surgical care of polyostotic fibrous dysplasia, the role of grafting ...

Polyostotic fibrous dysplasia.

An 18-year-old man was referred to the authors' institution's thoracic cancer specialists for further consultation after abnormal findings were seen on chest radiograph.

Monostotic fibrous dysplasia of the thoracic spine.

Fibrous dysplasia involving the thoracic spine is very rare. This patient had monostotic fibrous dysplasia involving the vertebral body, posterior elements, and right seventh rib with focal neurologic signs. The radiographic and bone scan findings are shown. The patient was treated successfully with tumor resection and arthrodesis using combined anterior and posterior approaches. Although fibro...

Aneurysmal bone cyst concomitant with fibrous dysplasia in the frontal bone.

Secondary aneurysmal bone cyst in fibrous dysplasia is exceedingly rare, especially in the skull and particularly in the frontal bone. We present a case of aneurysmal bone cyst concomitant with fibrous dysplasia in the frontal bone in a 15-year-old male patient presenting with headache and euphoria with an uncharacteristic imaging appearance and treated successfully by total resection.

[Polyostotic fibrous dysplasia: Albright's syndrome].